Online Formulary
  • Using the Formulary
  • Therapeutic Sections
    • 1. Gastro-intestinal system
    • 2. Cardiovascular system
    • 3. Respiratory
    • 4. Nervous system
    • 5. Infection
    • 6. Endocrine system
    • 7. Genito-urinary system
    • 8. Immune System
    • 8. Malignant disease
    • 9. Blood and blood-forming organs
    • 9. Nutrition and metabolic disorders
    • 10. Musculoskeletal system
    • 11. Eye
    • 12. Ear
    • 12. Nose
    • 12. Oropharynx
    • 13. Skin
    • 14. Vaccines
    • 15. Anaesthesia
    • 16. Emergency Treatment of Poisoning
    • Palliative Care
    • Wound management products
    • Stoma products
    • Continence products
    • Borderline substances
    • General recommendations and information
    • Shared Care
  • Using the Formulary
  • Therapeutic Sections
    • 1. Gastro-intestinal system
    • 2. Cardiovascular system
    • 3. Respiratory
    • 4. Nervous system
    • 5. Infection
    • 6. Endocrine system
    • 7. Genito-urinary system
    • 8. Immune System
    • 8. Malignant disease
    • 9. Blood and blood-forming organs
    • 9. Nutrition and metabolic disorders
      • 9.5 Fluid and electrolyte imbalances
      • 9.6 Metabolic disorders
        • 9.6.1 Acute porphyrias
        • 9.6.2 Carnitine deficiency
        • 9.6.3 Cystinosis
        • 9.6.4 Fabry's disease
        • 9.6.5 Gaucher's disease
        • 9.6.6 Homocystinuria
        • 9.6.7 Hypophosphatasia
        • 9.6.8 Mucopolysaccharidosis
        • 9.6.9 Niemann-pick type c disease
        • 9.6.10 Pompe disease
        • 9.6.11 Tyrosinaemia type i
        • 9.6.12 Urea cycle disorders
        • 9.6.13 Wilson's disease
      • 9.7 Mineral and trace elements deficiencies
      • 9.8 Nutrition (intravenous)
      • 9.9 Nutrition (oral)
      • 9.10 Vitamin deficiency
      • Local recommendations (Nutrition)
    • 10. Musculoskeletal system
    • 11. Eye
    • 12. Ear
    • 12. Nose
    • 12. Oropharynx
    • 13. Skin
    • 14. Vaccines
    • 15. Anaesthesia
    • 16. Emergency Treatment of Poisoning
    • Palliative Care
    • Wound management products
    • Stoma products
    • Continence products
    • Borderline substances
    • General recommendations and information
    • Shared Care
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Drug Status Key

  • On Formulary
  • Specialist Initiation

    On formulary but requires initiation by a specialist. 
    GPs may then take on maintenance prescribing - 
    Using the Formulary (eastkentformulary.nhs.uk)

  • Shared Care
  • Hospital Only
  • Not Recommended

Preferences

  • First Line
  • Second Line
  • Third Line
  • No Preference

9.6.4 Fabry's disease

Expand All / Expand All (incl. cost)

Agalsidase beta

NICE EMC

Agalsidase beta 35mg powder for solution for infusion vials

Pack Price
1 vial

Alglucosidase alfa

NICE EMC

Alglucosidase alfa 50mg powder for solution for infusion vials

Pack Price
1 vial

Online Formulary by M.O.M. Systems

NICE guidance is available from https://www.nice.org.uk/guidance All rights reserved. Subject to Notice of rights.
NICE guidance is prepared for the National Health Service in England. All NICE guidance is subject to regular review and may be updated or withdrawn. NICE accepts no responsibility for the use of its content in this product/publication.

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